Scrotoschisis: A Rare External Genital Anomaly - A Case Report
Keywords:
Scrotoschisis, Ectopic, Testes, Extracorporeal, Neonatal, SurgeryAbstract
Background: Scrotoschisis is a rare congenital abnormality of the external genitalia where the testis is exteriorized through an opening in the scrotal wall. Despite unknown aetiology various theories have been proposed for its occurrence. We report a case of a 3-day-old male presenting with an eviscerated left testis, exploring possible aetiologic hypotheses and management considerations. Successful surgical intervention resulted in good outcome.
Aim/objective: To outline the essential steps in the diagnosis and management of this rare congenital anomaly and to explore the possible aetiologic hypotheses in literature.
Case Report: A 3-day old male weighing 3.05 kg delivered vaginally in a rural health centre to a forty-year-old gravida 4 para 3 mother at 39 weeks’ gestation was brought to the Sick Baby Unit with an abnormal protrusion of flesh from a left hemiscrotal defect, noticed at birth. Nil significant associated perinatal history. General examination and vital signs reveal essentially normal findings. There was a 2.0 x 1.5 cm defect on the anteromedial surface of the left hemiscrotum, through which the left testis, epididymis and spermatic cord protruded. The exposed testis and spermatic cord were oedematous, covered with granulation tissue but appears viable in colour with good testicular artery pulsations. The contralateral testis was normally descended within the right hemiscrotum. A diagnosis of left Scrotoschisis was made. Patient was admitted, informed consent obtained, prepared and had operative reduction/fixation of the testis with closure of the scrotal defect.
Conclusion: Scrotoschisis is a rare congenital defect of the external genitalia, occurring mostly in term male newborns. Early recognition and prompt surgical treatment are essential in managing scrotoschisis and preventing testicular injury.
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